Rapidly evolving cryoglobulinemic vasculitis
Keywords:
vasculitis, cryoglobulinemia
Abstract
Vasculitis is manifested by inflammation of the blood vessels, affecting from the capillaries to the largest vessels. Dermatological compromise due to vasculitis ranges from mild cases that generate superficial involvement to ulcers and necrosis of different tissues. Cryoglobulinemia is characterized by the presence of serum cryoglobulins, which precipitate at temperatures below 37 degrees Celsius. It is associated with infectious, immune-mediated, and lymphoproliferative diseases, especially infection by the hepatitis C virus. Vasculitis in the context of cryoglobulins is produced by immune complex deposits in capillaries, arterioles, and small and medium-sized arteries. Treatment is based on treating the underlying cause and modulating the inflammatory response. We present the case of a 50-year-old man, with a history of chronic hepatitis B, who presented acute and critical ischemia of both extremities, documenting cryoglobulinemic vasculitis with poor evolution.References
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Published
2023-11-27
How to Cite
1.
Rodríguez Arias EA, Sigismondo MS, de Arza Pochylak L, Díaz Aguiar P, Loayza Reynolds GB. Rapidly evolving cryoglobulinemic vasculitis. Rev. Argent. Reumatol. [Internet]. 2023Nov.27 [cited 2024Sep.16];34(3). Available from: https://ojs.reumatologia.org.ar/index.php/revistaSAR/article/view/777
Section
Clinical Case
Copyright (c) 2023 on behalf of the authors. Reproduction rights: Argentine Society of Rheumatology
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.
