Un caso de afectación cutánea severa en la presentación clínica inicial de una dermatomiositis juvenil

Teresa Cristina Martins Vicente Robazzi; Celina Bulhões; Leandra Chaves; Cristiani Leal

doi:10.47196/rar.v28i3.557

Teresa Cristina Martins Vicente Robazzi Universidad Federal de Bahia, Salvador, Brasil
Celina Bulhões Hospital Profesor Edgar Santos, Salvador, Brasil
Leandra Chaves Hospital Profesor Edgar Santos, Salvador, Brasil
Cristiani Leal Hospital Profesor Edgar Santos, Salvador, Brasil

DOI: https://doi.org/10.47196/rar.v28i3.557

Palabras clave: dermatomiositis juvenil, presentación inicial

Resumen

La dermatomiositis juvenil es una colagenopatía que afecta a niños y adolescentes, princi-palmente entre las edades de 4 y 16 años. Sus principales manifestaciones clínicas son la debilidad simétrica de músculos proximales, enzimas musculares elevadas y la presencia de lesiones cutáneas, como el heliotropo y las pápulas de Gottron. Aquí describimos un caso de dermatomiositis juvenil con un inicio precoz a los 18 meses de edad, presentando lesiones cutáneas ulcerativas severas y vasculopatía probablemente debido a la afectación gastroin-testinal, que requirió tratamiento inmediato con inmunosupresores.

Biografía del autor/a

Teresa Cristina Martins Vicente Robazzi, Universidad Federal de Bahia, Salvador, Brasil

Facultad de Medicina. Departamento de Pediatría

Celina Bulhões, Hospital Profesor Edgar Santos, Salvador, Brasil

Reumatología Pediátrica

Leandra Chaves, Hospital Profesor Edgar Santos, Salvador, Brasil

Reumatología Pediátrica

Cristiani Leal, Hospital Profesor Edgar Santos, Salvador, Brasil

Reumatología Pediátrica

Citas

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