Un caso de afectación cutánea severa en la presentación clínica inicial de una dermatomiositis juvenil

  • Teresa Cristina Martins Vicente Robazzi Universidad Federal de Bahia, Salvador, Brasil
  • Celina Bulhões Hospital Profesor Edgar Santos, Salvador, Brasil
  • Leandra Chaves Hospital Profesor Edgar Santos, Salvador, Brasil
  • Cristiani Leal Hospital Profesor Edgar Santos, Salvador, Brasil
Palabras clave: dermatomiositis juvenil, presentación inicial

Resumen

La dermatomiositis juvenil es una colagenopatía que afecta a niños y adolescentes, princi-palmente entre las edades de 4 y 16 años. Sus principales manifestaciones clínicas son la debilidad simétrica de músculos proximales, enzimas musculares elevadas y la presencia de lesiones cutáneas, como el heliotropo y las pápulas de Gottron. Aquí describimos un caso de dermatomiositis juvenil con un inicio precoz a los 18 meses de edad, presentando lesiones cutáneas ulcerativas severas y vasculopatía probablemente debido a la afectación gastroin-testinal, que requirió tratamiento inmediato con inmunosupresores.

Biografía del autor/a

Teresa Cristina Martins Vicente Robazzi, Universidad Federal de Bahia, Salvador, Brasil
Facultad de Medicina. Departamento de Pediatría
Celina Bulhões, Hospital Profesor Edgar Santos, Salvador, Brasil
Reumatología Pediátrica
Leandra Chaves, Hospital Profesor Edgar Santos, Salvador, Brasil
Reumatología Pediátrica
Cristiani Leal, Hospital Profesor Edgar Santos, Salvador, Brasil
Reumatología Pediátrica

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Publicado
2017-09-01
Cómo citar
1.
Martins Vicente Robazzi TC, Bulhões C, Chaves L, Leal C. Un caso de afectación cutánea severa en la presentación clínica inicial de una dermatomiositis juvenil. Rev. Argent. Reumatol. [Internet]. 1 de septiembre de 2017 [citado 29 de marzo de 2024];28(3):33 -7. Disponible en: https://ojs.reumatologia.org.ar/index.php/revistaSAR/article/view/557